A mutation in the NADH-dehydrogenase subunit 2 suppresses fibroblast aging

Journal Publication ResearchOnline@JCU
Schauer, Marianne;Kottek, Tina;Schönherr, Madeleine;Bhattacharya, Animesh;Ibrahim, Saleh M.;Hirose, Misa;Köhling, Rüdiger;Fuellen, Georg;Schmitz, Ulf;Kunz, Manfred
Abstract

Mutations of mitochondrial (mt)DNA cause a variety of human diseases and are implicated in premature aging syndromes. Here we investigated a single nucleotide exchange (leucine to methionine) at position nt4738 in the mitochondrial NADH dehydrogenase subunit 2 (Nd2) gene of the respiratory chain. Primary fibroblasts derived from the conplastic mouse strain C57BL/6J-mtALR/LTJ with mutant enzyme, possessed high enzyme activity and ATP production and low ROS production. Furthermore, Nd2-mutant fibroblasts expressed lower senescence markers. Transcriptome analysis revealed that the members of the p38MAPK pathway were significantly downregulated in Nd2-mutant mice. In agreement, inhibition of p38MAPK with SB203580 enhanced proliferation and reduced cytokine secretion in fibroblasts. In Nd2-mutant mouse skin, the amount of Ki67-positive cells was significantly higher than in control skin. The higher amount of Ki67-positive cells and the thicker epidermis in Nd2-mutant mice strongly supported the in vitro data. In conclusion, Nd2 is a mitochondrial gene, involved in age-related signaling pathways.

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Oncotarget

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6

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1949-2553

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15

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Impact Journals

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